Abstract
It is an infrequent congenital pathology in pediatrics when children are born with an open malformation. Bladder exstrophy is a rare congenital pathology manifests itself as isolated defect or as part of several defects as a complex. We present a clinical case of nine-month-old baby girl suffered from absence of anterior abdominal wall and anterior bladder wall, divergence of bones pelvic articulation and absence of anus. The congenital defect was detected intrauterine by ultrasound at the third screening. After birth, an operation with a colostomy was performed. Due to the severe diagnosis, a decision was made to hospitalize her at our medical facility for further examination and treatment.