Modern Methods of Surgical Treatment of Osteogenesis Imperfecta in Children: a Literature Review

2022

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DOI 10.52889/1684-9280-2022-4-65-26-31
Data confidence 70 medium
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Abstract

Osteogenesis imperfecta is a widespread hereditary dysplasia of connective tissue, characterized by changes in the bone structure, frequent fractures, manifestations of disorders in other organs and systems. This is a genetically determined disease, characterized by a violation of the production of collagen type 1, for which a specific treatment algorithm has not yet been developed.The article presents scientific data on modern methods of surgical treatment of osteogenesis imperfecta in children using non-telescopic and telescopic intramedullary pins (Rusch nail, titanium elastic rods (TEN), etc.). The article also describes the shortcomings and expected complications after surgical treatment using these metal structures.Key words: incomplete osteogenesis, children, surgical treatment, osteosynthesis, osteotomy, rods.