Аннотация
Congenital epidermolysis bullosa is a rare disease. The main symptom of the disease is the formation of bubbles, even after minor mechanical trauma to the skin. The severity of disease is reduced to the period of puberty. Extreme difficulties arise in the case of additional diseases that require surgical intervention. Physician should choose a rational type of tactics of the patient treatment in order to eliminate the pathological process with minimal aggravation of the patient's condition on the underlying disease. Child G., 4 months entered on 16.09.11 complaining of the presence of the skin all over the body and limbs ulcers covered with crusts, at different stages of healing, difficult urinating. He is observed by a dermatologist with a diagnosis of “congenital epidermolysis bullosa”. Surgeon in outpatient terms performed the autopsy of education, treatment, subsequently observed the formation of scar phimosis with difficult urinating. Foreskin deformed, expressed edema and hyperemia of tissues, hole of the foreskin is narrowed due to the formed scar here ‐ the continuing phase of wound healing with the development of granulation growths. Surgical intervention for emergency indications was performed to resolve acute urinary retention, restore of spontaneous urination ‐ circular excision of the foreskin with the removal of the pathological process leading to the development of urinary retention, it was used during the operation a principle of minimal soft tissue injury with the exception of the forceps, clamp to hold penis in position used gauze soaked in glycerine. Results The child was discharged on the 6th day in a satisfactory condition. He is examined in a month ‐ no complications noted, the process of urination is not broken. (Valeologia j. №3 2014)