Аннотация
Annotation Fibrous dysplasia is a rare tumor-like condition characterized by the replacement of normal bone with fibrous tissue, with an etiology of uncertain origin. Diagnosis relies on clinical and radiological data, with biopsies used in doubtful cases. The aim of our study is to demonstrate our experience in working with a rare pathology such as fibrous dysplasia of the pterygoid process. We report a clinical case of isolated fibrous dysplasia affecting the pterygoid process of the left sphenoid bone, treated in the Pediatric Head and Neck Surgery Department of the University Medical Center, Astana, Kazakhstan. The patient, a 15-year-old girl, presented with a diagnosis of fibrous osteodysplasia of the left pterygoid process of the sphenoid bone. As a result of surgical treatment, we did not observe an increase in the tumor during a 3-year follow-up. Diagnosis of some tumors, such as fibrous dysplasia, is difficult and requires modern diagnostic methods. The presence of fibrous dysplasia in the sphenoid bone is a caustic pathology, which makes this clinical case unique. In this case, we used transnasal endoscopic approaches, which demonstrated the effectiveness of the treatment.